ABSTRACT
Dentinogenesis imperfecta [DI] associated with osteogenesis imperfecta [DI] is a genetic disorder that affects the connective tissues and results in dentine dysplasia. This case report dis [DI]; cusses the systemic and dental manifestations of DI and DI in a 4-year-old child, with moderate presentation of both disorders, who was treated at King Fahd Military Medical Complex in Dhah- ran. Dental treatment included the use of strip and stainless-steel crowns under local anesthesia, as; well as behavior modification techniques. Rigorous home care instructions, including reinforcement of the oral hygiene practice and avoidance of any episode that may lead to bone fracture, were disscussed with the parents. The case was reevaluated at 3-month follow-up visits, wherein the medical and dental histories were updated, the child's growth was monitored, periodic clinical and radio-graphic examinations were performed, and the oral hygiene was evaluated via the debris index score and caries risk assessment. Further treatment of the permanent dentition may be needed in the future